Interscapular-thoracic amputation: A giant Dermatofibrosarcoma Protuberans treatment

Background: Dermatofibrosarcoma protuberans (DFSP), an uncommon sarcoma of the dermis, is a low-grade, spindle-cell tumor that usually grows slowly and has a high local recurrence rate, but rarely metastasizes to distant sites. The diagnosis is based on histopathology and the standard treatment is...

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Bibliographic Details
Main Authors: De Anda Coronado, Alberto, López Leonar, Nohemí C., Navarro Bahena, Eduardo, Muñoz Maldonado, Gerardo Enrique
Format: Article
Language:English
Published: Erciyes University, Faculty of Medicine 2022
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Online Access:http://eprints.uanl.mx/28225/1/756.pdf
Description
Summary:Background: Dermatofibrosarcoma protuberans (DFSP), an uncommon sarcoma of the dermis, is a low-grade, spindle-cell tumor that usually grows slowly and has a high local recurrence rate, but rarely metastasizes to distant sites. The diagnosis is based on histopathology and the standard treatment is wide surgical excision with tumor-free margins. Case Report: Described is the case of a 75-year-old female who presented with a giant tumor on her upper right arm that had been increasing in size for a year. A biopsy provided the diagnosis of DFSP. Radical surgery was performed and the arm was disarticulated from the scapula. Conclusion: Treatment for DFSP typically involves surgical excision; however, the size of the tumor in the present case was exceptionally large. Disarticulation offered the best prognosis.