Bullous mastocytosis mimicking congenital epidermolysis bullosa
A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters assoc...
Autores principales: | , , |
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Formato: | Artículo |
Lenguaje: | inglés |
Publicado: |
2014
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Materias: | |
Acceso en línea: | http://eprints.uanl.mx/15244/1/348.pdf |
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author | Salas Alanís, Julio César Rosales Mendoza, Cesar Eduardo Ocampo Candiani, Jorge |
author_facet | Salas Alanís, Julio César Rosales Mendoza, Cesar Eduardo Ocampo Candiani, Jorge |
author_sort | Salas Alanís, Julio César |
collection | Repositorio Institucional |
description | A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy
showing subepidermal blisters associated with a dermal infiltrate of Giemsa-positive cells and CD117-positive antibody was consistent with the diagnosis of bullous mastocytosis. Treatment with oral antihistamines, topical steroids, and antibiotics was initiated, leading to a
remission of the lesions. |
format | Article |
id | eprints-15244 |
institution | UANL |
language | English |
publishDate | 2014 |
record_format | eprints |
spelling | eprints-152442022-04-07T22:00:23Z http://eprints.uanl.mx/15244/ Bullous mastocytosis mimicking congenital epidermolysis bullosa Salas Alanís, Julio César Rosales Mendoza, Cesar Eduardo Ocampo Candiani, Jorge RL Dermatología A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters associated with a dermal infiltrate of Giemsa-positive cells and CD117-positive antibody was consistent with the diagnosis of bullous mastocytosis. Treatment with oral antihistamines, topical steroids, and antibiotics was initiated, leading to a remission of the lesions. 2014 Article PeerReviewed text en cc_by_nc_nd http://eprints.uanl.mx/15244/1/348.pdf http://eprints.uanl.mx/15244/1.haspreviewThumbnailVersion/348.pdf Salas Alanís, Julio César y Rosales Mendoza, Cesar Eduardo y Ocampo Candiani, Jorge (2014) Bullous mastocytosis mimicking congenital epidermolysis bullosa. Case reports in dermatology, 6 (2). pp. 129-133. ISSN 1662-6567 http://doi.org/10.1159/000362755 doi:10.1159/000362755 |
spellingShingle | RL Dermatología Salas Alanís, Julio César Rosales Mendoza, Cesar Eduardo Ocampo Candiani, Jorge Bullous mastocytosis mimicking congenital epidermolysis bullosa |
thumbnail | https://rediab.uanl.mx/themes/sandal5/images/online.png |
title | Bullous mastocytosis mimicking congenital epidermolysis bullosa |
title_full | Bullous mastocytosis mimicking congenital epidermolysis bullosa |
title_fullStr | Bullous mastocytosis mimicking congenital epidermolysis bullosa |
title_full_unstemmed | Bullous mastocytosis mimicking congenital epidermolysis bullosa |
title_short | Bullous mastocytosis mimicking congenital epidermolysis bullosa |
title_sort | bullous mastocytosis mimicking congenital epidermolysis bullosa |
topic | RL Dermatología |
url | http://eprints.uanl.mx/15244/1/348.pdf |
work_keys_str_mv | AT salasalanisjuliocesar bullousmastocytosismimickingcongenitalepidermolysisbullosa AT rosalesmendozacesareduardo bullousmastocytosismimickingcongenitalepidermolysisbullosa AT ocampocandianijorge bullousmastocytosismimickingcongenitalepidermolysisbullosa |