Bullous mastocytosis mimicking congenital epidermolysis bullosa

A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters assoc...

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Detalles Bibliográficos
Autores principales: Salas Alanís, Julio César, Rosales Mendoza, Cesar Eduardo, Ocampo Candiani, Jorge
Formato: Artículo
Lenguaje:inglés
Publicado: 2014
Materias:
Acceso en línea:http://eprints.uanl.mx/15244/1/348.pdf
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author Salas Alanís, Julio César
Rosales Mendoza, Cesar Eduardo
Ocampo Candiani, Jorge
author_facet Salas Alanís, Julio César
Rosales Mendoza, Cesar Eduardo
Ocampo Candiani, Jorge
author_sort Salas Alanís, Julio César
collection Repositorio Institucional
description A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters associated with a dermal infiltrate of Giemsa-positive cells and CD117-positive antibody was consistent with the diagnosis of bullous mastocytosis. Treatment with oral antihistamines, topical steroids, and antibiotics was initiated, leading to a remission of the lesions.
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spelling eprints-152442022-04-07T22:00:23Z http://eprints.uanl.mx/15244/ Bullous mastocytosis mimicking congenital epidermolysis bullosa Salas Alanís, Julio César Rosales Mendoza, Cesar Eduardo Ocampo Candiani, Jorge RL Dermatología A 2-month-old female infant was referred to DebRA Mexico from the Regional Children’s Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters associated with a dermal infiltrate of Giemsa-positive cells and CD117-positive antibody was consistent with the diagnosis of bullous mastocytosis. Treatment with oral antihistamines, topical steroids, and antibiotics was initiated, leading to a remission of the lesions. 2014 Article PeerReviewed text en cc_by_nc_nd http://eprints.uanl.mx/15244/1/348.pdf http://eprints.uanl.mx/15244/1.haspreviewThumbnailVersion/348.pdf Salas Alanís, Julio César y Rosales Mendoza, Cesar Eduardo y Ocampo Candiani, Jorge (2014) Bullous mastocytosis mimicking congenital epidermolysis bullosa. Case reports in dermatology, 6 (2). pp. 129-133. ISSN 1662-6567 http://doi.org/10.1159/000362755 doi:10.1159/000362755
spellingShingle RL Dermatología
Salas Alanís, Julio César
Rosales Mendoza, Cesar Eduardo
Ocampo Candiani, Jorge
Bullous mastocytosis mimicking congenital epidermolysis bullosa
thumbnail https://rediab.uanl.mx/themes/sandal5/images/online.png
title Bullous mastocytosis mimicking congenital epidermolysis bullosa
title_full Bullous mastocytosis mimicking congenital epidermolysis bullosa
title_fullStr Bullous mastocytosis mimicking congenital epidermolysis bullosa
title_full_unstemmed Bullous mastocytosis mimicking congenital epidermolysis bullosa
title_short Bullous mastocytosis mimicking congenital epidermolysis bullosa
title_sort bullous mastocytosis mimicking congenital epidermolysis bullosa
topic RL Dermatología
url http://eprints.uanl.mx/15244/1/348.pdf
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